Retroperitoneal Malignant Peripheral Nerve Sheath Tumour: A Rare Case Report

DEĞER A. N., BAYAR M. A., ÇAYDERE M., DEĞER H., TAYFUR M.

JOURNAL OF CLINICAL AND DIAGNOSTIC RESEARCH, cilt.9, sa.9, 2015 (ESCI, Scopus) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 9 Sayı: 9
  • Basım Tarihi: 2015
  • Doi Numarası: 10.7860/jcdr/2015/14169.6481
  • Dergi Adı: JOURNAL OF CLINICAL AND DIAGNOSTIC RESEARCH
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, Academic Search Premier, EMBASE, Directory of Open Access Journals
  • Erzincan Binali Yıldırım Üniversitesi Adresli: Evet

Özet

Malignant nerve sheath tumours (MPNST) are rare neoplasias and retroperitoneal cases are fairly rare and clinically difficult to be detected, but they are very agressive neoplasias. MPNST are frequently seen in head, neck and upper extremities. In patients with NF1; MPNST, a poor-prognostic lesion, may result from a malignant degeneration of a former plexiform neurofibroma. It is necessary to be aware of a potential malignancy in patients diagnosed with plexiform neurofibroma.